DEDIFFERENTIATED CHORDOMA WITH A SARCOMATOUS COMPONENT: AN OVERLOOKED DIAGNOSIS

Authors

  • Quratulain Masood
  • Mohammad Bilal
  • Ayesha Tariq
  • Somal Khan
  • Asad Qureshi

Abstract

A 60 year old male presented with unremitting complaints of acute urinary retention andconstipation. Computerized Tomography of the abdomen and pelvis confirmed a sacral mass. Thebiopsy diagnosed dedifferentiated sacral chordoma; an extremely rare entity, seldom reported andfrequently misdiagnosed. We present a unique case report after an extensive review ofretrospective literature on dedifferentiated chordomas.Keywords: Chordomas, Dedifferentiated chordomas, Sacral chordomas, Malignant fibroushistiocytoma

References

Pal DK, Chowdhury MK. Sacro-coccygeal chordoma: An

unusual cause of retention of urine. Indian J Urol

;20:170–1.

Carbone A, Gezeroglu H, Ciccariello M, Aloisi P, Martis G.

[Does the neurologic assessment have a decisive role in the

early diagnosis of urinary disorders of uncertain etiology? A

case of spinal chordoma] Arch Ital Urol Androl

;71(1):37–9

Sahasrabudhe NS, Jadhav MV, Holla VV. Dedifferentiated

chordoma – a case report. Indian J Pathol Microbiol

;45:353–4.

Saito A, Hasegawa T, Shimoda T, Toda G, Hirohashi S,

Tajima G, et al. Dedifferentiated chordoma: a case report.

Jpn J Clin Oncol 1998;28(12):766–71

Kaiser TE, Pritchard DJ, Unni KK. Clinicopathologic study

of sacrococcygeal chordoma. Cancer 1984;53:2574–8.

Ozaki T, Hillmann A, Winkelmann W. Surgical treatment of

sacrococcygeal chordoma. J Surg Oncol 1997;64:274–9.

Bergh P, Kindblom LG, Gunterberg B, Remotti F, Ryd W,

Meis-Kindblom JM. Prognostic factors in chordoma of the

sacrum and mobile spine: a study of 39 patients. Cancer

;88:2122–34.

Published

2009-03-01