• Alyscia M Cheema Department of Opthalmology, Jinnah Post Graduate Medical Centre, Karachi
  • Nausheen Hayat Department of Opthalmology, Jinnah Post Graduate Medical Centre, Karachi


Naevus Sebaceous of Jadassohn is a rarely seen hamartomatous lesion and is a fourth type of sebaceous gland tumour, in which sebaceous glands show nevoid character of growth composed partly or completely of sebaceous glands. A detailed research revealed that very little data is available; no case of this disorder has been reported as an isolated eye lid lesion. Majority of the published cases are associated with systemic involvement. We present here a case report of this rare disorder. A middle age female patient presented with a mass of left lower lid since childhood without any other ocular and systemic abnormality. Excision biopsy along with rotation flap surgery was done. Histopathological examination of the specimen revealed the diagnosis. To our best of knowledge this is a unique presentation of naevus sebaceous of Jadassohn on eye lid which has not been documented till yet anywhere


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