UNUSUAL INITIAL PRESENTATION OF PRIMARY ANTIPHOSPHOLIPID SYNDROME AS POSTPARTUM SYMMETRICAL PERIPHERAL GANGRENE

Authors

  • Marium Marufia Khan Dr Ruth Pfau Civil Hospital Karachi-Pakistan
  • Sana Shahid Dr Ruth Pfau Civil Hospital Karachi-Pakistan
  • Amara Zafar Dr Ruth Pfau Civil Hospital Karachi
  • Nudrat Naz Khan Dr Ruth Pfau Civil Hospital Karachi-Pakistan
  • Shaheen Bhatty Dr Ruth Pfau Civil Hospital Karachi-Pakistan

Abstract

Antiphospholipid syndrome (APS) is an acquired prothrombic state with recurring thromboembolic and obstetric complications in the presence of antiphospholipid antibodies. Isolated skin manifestation especially symmetrical peripheral gangrene (SPG) in postpartum phase is reported rarely. To highlight this unusual presentation of APS with SPG we present a case of young female who developed SPG on her third postpartum day. Postpartum period runs a high risk of sepsis but development of such extensive and rapid ischemic changes in APS is seen uncommonly.

References

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Published

2022-01-01