DEDIFFERENTIATED CHORDOMA WITH A SARCOMATOUS COMPONENT: AN OVERLOOKED DIAGNOSIS

Quratulain Masood, Mohammad Bilal, Ayesha Tariq, Somal Khan, Asad Qureshi

Abstract


A 60 year old male presented with unremitting complaints of acute urinary retention and
constipation. Computerized Tomography of the abdomen and pelvis confirmed a sacral mass. The
biopsy diagnosed dedifferentiated sacral chordoma; an extremely rare entity, seldom reported and
frequently misdiagnosed. We present a unique case report after an extensive review of
retrospective literature on dedifferentiated chordomas.
Keywords: Chordomas, Dedifferentiated chordomas, Sacral chordomas, Malignant fibrous
histiocytoma

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