A PUZZLING CASE OF SEVERE PULMONARY HYPERTENSION - A CASE REPORT

Authors

  • Muhammad Sohaib Arif National Institute of Cardiovascular Disease (NICVD), Karachi-Pakistan
  • Ali Ammar National Institute of Cardiovascular Disease (NICVD), Karachi-Pakistan
  • Usman Tauseef National Institute of Cardiovascular Disease (NICVD), Karachi-Pakistan
  • Abdul Hakeem Shaikh National Institute of Cardiovascular Disease (NICVD), Karachi-Pakistan
  • Abdul Sattar Shaikh National Institute of Cardiovascular Disease (NICVD), Karachi-Pakistan
  • Jawed Abubaker National Institute of Cardiovascular Disease (NICVD), Karachi-Pakistan

DOI:

https://doi.org/10.55519/JAMC-01-13355

Keywords:

pulmonary hypertension, diaphragm paralysis, non-invasive ventilation, pericardectomy, constrictive pericarditis, tuberculosis

Abstract

Pulmonary hypertension (PH) is a life-threatening cardiopulmonary disorder marked by elevated pressure in the pulmonary arteries. We report a 51-year-old male, post-pericardectomy, presenting with breathlessness. Diagnosis revealed pulmonary hypertension with depressed right ventricle function. Managed with non-invasive ventilation (NIV) and oxygen, he was slated for right heart angiography but couldn't lie flat. Fluoroscopy identified bilateral diaphragm paralysis. Due to a lack of diaphragm-related procedures, he continued non-invasive ventilation, oxygen, and pulmonary vasodilators. With these measures, the functional status of the patient improved and he was able to carry out his routine activities.

Author Biographies

Usman Tauseef, National Institute of Cardiovascular Disease (NICVD), Karachi-Pakistan

Correspondence:

National Institute of Cardiovascular Disease (NICVD), Karachi-Pakistan

Cell: +92 323 822 9360

Email: usman.tauseef.dr@gmail.com

Jawed Abubaker, National Institute of Cardiovascular Disease (NICVD), Karachi-Pakistan

  • Professor and Chairperson, Pulmonary and Critical care

References

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Published

2025-03-15

How to Cite

1.
Arif MS, Ammar A, Tauseef U, Shaikh AH, Shaikh AS, Abubaker J. A PUZZLING CASE OF SEVERE PULMONARY HYPERTENSION - A CASE REPORT. J Ayub Med Coll Abbottabad [Internet]. 2025 Mar. 15 [cited 2025 Aug. 31];37(1):196-8. Available from: https://jamc.ayubmed.edu.pk/index.php/jamc/article/view/13355

Issue

Vol. 37 No. 1 (2025): JOURNAL OF AYUB MEDICAL COLLEGE ABBOTTABAD

Section

CASE REPORT

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Copyright (c) 2025 Muhammad Sohaib Arif, Ali Ammar, Usman Tauseef, Abdul Hakeem Shaikh, Abdul Sattar Shaikh, Jawed Abubaker

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