SUBCUTANEOUS LEIOMYOSARCOMA OF SUPRA-PUBIC REGION MANAGED WITH WIDE LOCAL EXCISION AND TOTAL PENECTOMY

Authors

  • Syed Muhammad Nazim The Aga Khan University Hospital, stadium road, Karachi- 74800.
  • Ayesha Nusrat The Aga Khan University Hospital, Karachi Pakistan.
  • Ahmad Bashir Aga Khan University, Karachi

DOI:

https://doi.org/10.55519/JAMC-03-11083

Keywords:

Leiomyosarcoma, Subcutaneous, Abdominal wall, Surgery, Penectomy

Abstract

Subcutaneous leiomyosarcomas (LMS) are rare soft tissue sarcomas arising from small-to-medium-sized blood vessels. Involvement of the anterior abdominal wall is extremely rare. We present a case of a 72-year-old gentleman who presented with 3 months history of a progressively increasing mass in the supra-pubic region reaching the root of penis without any regional lymphadenopathy. Magnetic resonance imaging (MRI) pelvis showed a large heterogeneous mass in lower abdomen indenting the penile corpora. Complete pathological clearance was achieved by wide excision of the mass with total penectomy and cutaneous urethrostomy. The patient received adjuvant radiation therapy and is free of local recurrence or distant metastasis two years after the surgery.

Author Biography

Syed Muhammad Nazim, The Aga Khan University Hospital, stadium road, Karachi- 74800.

Assistant Professor, Department of Surgery, The Aga Khan University Hospital Karachi

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Published

2023-07-09