SCLEREDEMA DIABETICORUM; A RARE DISEASE

Authors

  • Amber Waqar Pakistan Institute of Medical Sciences, Islamabad-Pakistan
  • Saleh Khurshied Pakistan Institute of Medical Sciences, Islamabad-Pakistan
  • Mahvish Aftab Khan Pakistan Institute of Medical Sciences, Islamabad-Pakistan
  • Aisha Baloch Pakistan Institute of Medical Sciences, Islamabad-Pakistan
  • Mohammad Riaz Khan Pakistan Institute of Medical Sciences, Islamabad-Pakistan
  • Nawal Khurshid Pakistan Institute of Medical Sciences, Islamabad-Pakistan

DOI:

https://doi.org/10.55519/JAMC-01-12868

Keywords:

Scleredema diabeticorum, Pakistan, Cutaneous manifestations, Diabetes

Abstract

Scleredema Diabeticorum (SD) is a rare condition characterized by diffuse, symmetrical induration along with non-pitted swelling mostly on the upper back as a result of mucin being deposited in the dermis. It can also involve posterior neck, shoulders, and scalp. We report a case of 48 years old female patient from Pakistan, with uncontrolled diabetes mellites type 2 for the last 15 years, presenting with thickened skin at the back of the neck resulting in difficulty in neck and shoulder movements. This led to decreased functional class from I to II causing her to develop insomnia and depression. Scleredema diabeticorum is a difficult disease to manage as it runs a long and debilitating course with little propensity of remission with available treatments.

Author Biographies

Amber Waqar, Pakistan Institute of Medical Sciences, Islamabad-Pakistan

 

Saleh Khurshied, Pakistan Institute of Medical Sciences, Islamabad-Pakistan

 

Mahvish Aftab Khan, Pakistan Institute of Medical Sciences, Islamabad-Pakistan

 

Aisha Baloch, Pakistan Institute of Medical Sciences, Islamabad-Pakistan

 

Mohammad Riaz Khan, Pakistan Institute of Medical Sciences, Islamabad-Pakistan

 

Nawal Khurshid, Pakistan Institute of Medical Sciences, Islamabad-Pakistan

 

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Published

2024-04-17