STURGE WEBER SYNDROME-UNUSUAL PRESENTATION

Authors

  • N.S. Neki

Abstract

Sturge Weber Syndrome or encephalo-trigeminal angiomatosis is non-hereditary, congenital and rare disorder of unknown aetiology. It is characterised by vascular malformation with capillary venous angiomas involving face, eye and leptomeninges resulting in neurological and orbital manifestations. A case of 23 years old female presented with history of tonic-clonic convulsions, evidence of Port wine stain on face since birth, characteristic CT findings diagnosed as a case of Sturge Weber Syndrome is reported here for its rarity.Keywords: Sturge Weber Syndrome; Port -wine stain; Seizures

References

REFERENCES

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Published

2014-03-01

Issue

Vol. 26 No. 1 (2014): JOURNAL OF AYUB MEDICAL COLLEGE, ABBOTTABAD

Section

CASE REPORT

License

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