• Raja RA Raja
  • Khemani VD Khemani
  • Sheikh S Sheikh
  • Khan H Khan


Background: Craniosynostosis is the premature fusion of cranial vault sutures. The overallincidence is 3–5/10,000 live births. With multiple craniosynostoses, brain growth may be impededby the unyielding skull. Most cases of single suture involvement can be treated with linearexcision of suture. Involvement of multiple sutures or skull has usually required combined effortsof neurosurgeons and craniofacial surgeons. Methods: On the basis of visible skull deformity allpatients were admitted in the Department of Neurosurgery, Liaquat University Hospital,Jamshoro, Pakistan. Patients were examined for signs of raised ICP and other congenitaldeformities. The records of patients were maintained till follow up. Results: Twenty-sevenchildren were included in this study from 2002 to 2009. Age range was 1–6 years, boys were 18(66.6%), and girls were 9 (33.3%). The common suture affected was coronal 12 (44.4%). Twochildren with craniostenosis belonged to same family, and all presented with suture involvement.Three (11.1%) deaths occurred due to hypothermia (1), and blood loss (2). Conclusion: Earlydiagnosis, expert surgical techniques and per- and postoperative care for bleeding and temperatureregulation prevent mortality and morbidity.Keywords: Craniosynostosis, children, skull defects, suture


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