• Jawad Akhtar Gilani
  • Muhammad Iqbal
  • M. Rauf Khattak
  • Safoora Shahid


We present a 15-years old young child primarily presented to general surgeon for abdominal massand gross haematuria. His detailed imaging studies and other relevant investigations revealed thatit is a case of Paediatric Renal Cell carcinoma (RCC), which was clinically not associated withany of the known malignancies or syndromes. On detailed histo-pathological examination this wasreported as a special type of Pediatric RCC not fitting into clear cell, papillary, chromophobic,oncocytoma or collecting duct RCC.Keywords: RCC, VHL, IHC


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