EXTRA OSSEOUS PRIMARY EWING’S SARCOMA

Authors

  • Syed Asad Ali
  • Agha Taj Muhammad
  • Abdul Ghani Soomro
  • Akmal Jamal Siddiqui

Abstract

The case of 20 years old boy with an extra osseous Ewing’s sarcoma is described. He was initiallydiagnosed as a case of infiltrative malignant tumour of left suprarenal gland on the basis of preoperativeworkup but postoperative biopsy of surgically excised specimen confirmed Extra-osseous Ewing’sSarcoma (EES) suprarenal gland with no evidence of malignancy on skeletal scintiscan, bone marrowaspirate and histopathology. Suprarenal location of primary EES is unknown and probably has not beenreported in literature. We report a unique case of EES.Keywords: Ewing’s sarcoma, extra osseous, suprarenal gland, management

References

Angervall L, Enzinger FM. Extra skeletal neoplasm resembling

Ewing’s Sarcoma Cancer 1975;36:240–51.

Rud NP, Reiman HM, Pritchard DJ, Frassica FJ, Smithson WA.

Extraosseous Ewing’s Sarcoma –A study of 42 cases. Cancer

;64:1548–53.

Ladany M, Heinemann FS, Huvos AG, Hanumantha Rao P,

Chen Q, Jhanwar SC. Neural differentiation in small round cell

tumor of bone and soft tissue with the translocation t(11;22)

(q24;q12): An immunohistochemical study of 11 cases. Human

Pathol 1990;21:1245–51.

Miller ME, Emerson L, Clayton F, Bentz BG, Data RE, Salzman

KL, et al. Extraosseous Ewing’s sarcoma. J Clin Oncol

;25:4845–8.

Ambros IM, Ambros PF, Strehl S, Kovar H, Gadner H, SalzerKuntschik M. MIC2 is a specific marker for Ewing’s sarcoma

and peripheral primitive neuroectodermal tumors. Evidence for a

common histogenesis of Ewing’s sarcoma and peripheral

primitive neuroectodermal tumors from MIC2 expression and

specific chromosome aberration. Cancer 1991;67:1886–93.

Brehaut LE, Anderson LH, Taylor DA. Extraskeletal Ewing’s

Sarcoma: Diagnosis of a case by fine needle aspiration cytology.

Acta Cytol 1986;30:683–7.

Kara G: Spinal Cord Ewing’s sarcoma Metastasis: presentation

of one case. Ann Nucl Med 2004;18:623–6.

Bacci G, Balladelli A, Forni C, Ferrari S, Longhi A, Bacchini P,

et al. Adjuvant and neoadjuvant chemotherapy for Ewing

sarcoma family tumors in patients aged between 40 and 60:

report of 35 cases and comparison of results with 586 younger

patients treated with the same protocols in the same years. Cancer

;109:780–6.

Kolb EA, Kushner BH, Gorlick R, Laverdiere C, Healey JH,

LaQuaglia MP, et al. Long-term event-free survival after

intensive chemotherapy for Ewing’s family of tumors in children

and young adults. J Clin Oncol 2003;21:3423–30.

Moodley M, Jordaan A: Ewings sarcoma of the vulva ‒a case

report. Int J Gynecol Cancer 2005;15:1177–8.

Downloads

Published

2010-09-01

Most read articles by the same author(s)