• Muhammad Arif
  • Zafar Iqbal
  • Zia -ul- Islam


Background: Retinoblastoma is a malignant intraocular tumour of childhood, if not detected early, itresults in loss of eye as well as life. The Objective was to study the pattern of presentation ofRetinoblastoma in order to detect the disease at an earlier stage. It was conducted at Supra RegionalReferral Centre for Retinoblastoma, Department of Ophthalmology, Khyber Teaching Hospital,Peshawar, Pakistan from 1st July 1999 to 30th September 2002. Methods: Seventy patients wereregistered and admitted for diagnostic evaluation. After initial interview a proforma was filled abouthistory of disease. Examination under anaesthesia included indirect ophthalmoscopy with indentation.B-scan of the eye and CT scan of the Orbit was done when required. Results: Forty (57.14%) patientspresented with Leukocoria; other presentation included hyphaema, strabismus, proptosis, 56.48%patients presented in stage VB (Rees Elsworth classification). Conclusion: Early detection throughbetter understanding of presenting features of the disease and application of diagnostic skills can reducethe advanced stage of Retinoblastoma.Keywords: Retinoblastoma, Leukocoria, strabismus, proptosis, B-scan, Rees Elsworth classification


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