DELAYED ERUPTION IN CLEIDOCRANIAL DYSPLASIA

Authors

  • Sanaa Ahmed Sindh Institute of Oral Health Sciences
  • Maria Naz Shaheen Sindh Institute of Oral Health Sciences
  • Faisal Hameed Sindh Institute of Oral Health Sciences

Abstract

Cleidocranial dysplasia is a rare autosomal dominant disorder of bones mainly affecting bones formed by intra-membranous and endochondral ossification. It presents clinically as brachycephalic skull, frontal bossing, depressed nasal bridge, hypertelorism, delayed closure of fontanelles, delayed eruption of permanent teeth, missing clavicles and wide pelvis. It runs in families; sporadic cases are rarer. Just over than 1000 cases have been reported. We are presenting here 2 cases of cleidocranial dysplasia in siblings.Keywords: Cleidocranial Dysplasia; Supernumerary Tooth; Pseudarthrosis Of Clavicle; Congenital

Author Biographies

Sanaa Ahmed, Sindh Institute of Oral Health Sciences

BDS,MS (OMFS)Department of Oral Medicine

Maria Naz Shaheen, Sindh Institute of Oral Health Sciences

BDSDepartment of Oral Medicine

Faisal Hameed, Sindh Institute of Oral Health Sciences

BDS, FCPS(OMFS)Assistant Professor,Department of Oral and Maxillofacial Surgery

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Published

2020-07-19