CONGENITAL ISOLATED BILATERAL SOFT TISSUE SYNGNATHIA IN A 4-DAY OLD BABY BOY

Authors

  • Abul Khair Zalan Paediatric Dentistry, Pakistan Institute of Medical Sciences, Islamabad-Pakistan
  • Khadeejah Khalil Zubairy Paediatric Dentistry, Pakistan Institute of Medical Sciences, Islamabad-Pakistan
  • Manahil Niazi Paediatric Dentistry, Pakistan Institute of Medical Sciences, Islamabad-Pakistan
  • Hira Zaman University College of Dentistry,Lahore
  • Anser Maxood Paediatric Dentistry, Pakistan Institute of Medical Sciences, Islamabad-Pakistan
  • Anika Gul Sardar Begum Dental College, Peshawar.

Abstract

Congenital maxillomandibular syngnathia is characterized by fusion of jaws. Depending on the severity, it has a wide range of clinical presentations. It can be complete /incomplete and may be unilateral or bilateral. Primary concern in such patients is maintenance of airway and feeding difficulties. Therefore, early recognition and management is important to reduce nutritional, feeding, airway difficulties and growth-related problems in such new-borns. This case report presents a case of syngnathia in a 4-day infant with bilateral fusion of maxilla and mandible, leaving a small anterior portion. Early intervention was planned and the fusion was released to facilitate feeding. Good mouth opening was seen on 1week follow-up. Keywords: Congenital; Maxillomandibular fusion; Syngnathia; Synechiae

Author Biographies

Abul Khair Zalan, Paediatric Dentistry, Pakistan Institute of Medical Sciences, Islamabad-Pakistan

BDS, MDS Final year post graduate resident. Pediatric dentistry

Khadeejah Khalil Zubairy, Paediatric Dentistry, Pakistan Institute of Medical Sciences, Islamabad-Pakistan

BDS, House Officer. Pediatric dentistry

Manahil Niazi, Paediatric Dentistry, Pakistan Institute of Medical Sciences, Islamabad-Pakistan

BDS, House Officer. Pediatric dentistry

Hira Zaman, University College of Dentistry,Lahore

BDS, MDS, Registrar. Operative dentistry.

Anser Maxood, Paediatric Dentistry, Pakistan Institute of Medical Sciences, Islamabad-Pakistan

BDS, FRACDS, FICD, MSc. Dean of Pediatric dentistry.

Anika Gul, Sardar Begum Dental College, Peshawar.

BDS, FCPS post gradute resident. Pediatric dentistry.

References

Cerrati EW, Ahmed OH, Rickert SM. Isolated congenital maxillomandibular synechiae. Am J Otolaryngol 2015;36(5):707–9

Parkins GE, Boamah MO. Congenital maxillomandibular syngnathia: Case report. J Cranio-Maxillofac Surg 2009;37(5):276–8.

Burket LW. Congenital bony temporomandibular ankylosis and facial hemiatrophy: review of the literature and report of a case. J Am Med Ass 1936;106(20):1719–22.

Gartlan MG, Davies J,Smith RJ . Congenital oral synechiae. Ann Otol Rhinol Laryngol 1993;102(3):186–97.

James O, Ibikunle AA, Adeyemo WL, Ogunlewe MO, Ladeinde AL. Maxillomandibular syngth nathia in an adult Nigerian patient. J Clin Sci 2016;13(1):40–3.

Bali R, Sharma P, Jain S, Thapar D. Congenital fibrous maxillomandibular fusion. J Maxillofac Oral Surg 2010;9(3):277–9.

Ogino A, Onish K, Maruyama Y. Congenital oral synechia associated with cleft palate: Cleft palate medial synechia syndrome? Eur J Plast Surg 2005;27(7):338–40.

Dawson KH, Gruss JS, Myall RW. Congenital bony syngnathia. A proposed classification. Cleft Palate Craniofac J 1997;34(2):141–6.

Mathis VH. Übereinen fall von ernäunng-sschwierigkeitbeiconnatalersyngnathie. Deutsche Zahnäzliche Zeitschrift 1962;17:1167–71.

Mir MA, Iqbal S, Hafeez A, Zargar HR, Rasool A, Mohsin M, et al. Syngnathia without any other associated anomaly: a very rare case report. Internet J Plast Surg 2007;4(1):6.

Puvabanditsin S, Garrow E, Sitburana O, Avila FM, Nabong MY, Biswas A. Syngnathia and van der woude syndrome: A case report and literature review. Cleft Palate Craniofac J 2003;40(1):104–6.

Rogers GF, Greene AK, Oh AK, Robson C, Mulliken JB. Zygomaticotemporal synostosis: A rare cause of progressive facial asymmetry. Cleft Palate Craniofac J 2007;44(1):106–11.

Martín LP, Pérez MM, García EG, Martín-Moro JG, González JI, García MB. Atypical case of congenital maxillomandibular fusion with duplication of the craniofacial midline. Craniomaxillofac Trauma Reconstr 2011;4(2):113–20.

Mevada K, Gopalkrishna A. Intraoral synechiae with cleft palate in an older child: A case report and review of literature. J Cleft Lip Plata Craniofac Anomal 2016;3(1):46–9.

Panda S, Sikka K, Punj J. Sharma SC. Bilateral congenital alveolar synechiae-a rare cause of trismus. Maxillofac Plast Reconstr Surg 2016;38(1):8.

Downloads

Published

2021-02-21