DERMATOFIBROSARCOMA PROTUBERANS OF TRUNK IN A MALE PATIENT

Authors

  • Junaid Zia Hashmi Nishtar Medical University and Hospital Multan
  • Ammarah Ghafoor Nishtar Medical University and Hospital Multan
  • Masood ur Rauf Khan Hiraj Nishtar Medical University and Hospital Multan
  • Waseem Abbas Chaudhary Nishtar Medical University and Hospital Multan

DOI:

https://doi.org/10.55519/JAMC-02-8960

Abstract

Dermatofibrosarcoma protuberans is a rare cutaneous malignancy. Usual sites of origin are trunk and extremities. Aetiology of the condition is not well understood but a genetic basis is explained as a reciprocal translocation t (17l;22) (q22; q13). Distant metastasis is quite rare as it is mostly a locally advancing tumour. Histopathology is the most accurate investigation to make a diagnosis. Imaging is still required to rule out distant metastasis. Surgical excision is the treatment option for stage I tumours. Imatinib, a tyrosine kinase inhibitor, has shown promising results in management of locally advanced and metastatic disease.

Author Biographies

Junaid Zia Hashmi, Nishtar Medical University and Hospital Multan

Post Graduate Resident, General Surgery

Ammarah Ghafoor, Nishtar Medical University and Hospital Multan

Post Graduate Resident , Dermatology

Masood ur Rauf Khan Hiraj, Nishtar Medical University and Hospital Multan

Professor of Surgery, Head Of Department

Waseem Abbas Chaudhary, Nishtar Medical University and Hospital Multan

Senior Registrar, General Surgery

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Published

2022-03-03

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