• Danish Abdul Aziz Aga Khan University Hospital Karachi, Pakistan
  • Fozia Memon chief Resident Aga khan University Hospital
  • Arshalooz Rahman Aga Khan University Hospital Karachi Pakistan
  • Madiha Ali Intern Aga khan University Hospital Karachi Pakistan


Hypertension in paediatric age group is commonly secondary to a known cause. It is crucial to identify the cause of hypertension and treat it before development of any associated complications to prevent morbidity and mortality. Paediatric Hypertension is one of the important clinical finding in a child with certain clinical syndrome. We are presenting a case of a 10 month old child presenting with hypertension and hypokalaemia, after excluding all identifiable causes and her positive response to therapy, that is amiloride, along with supportive biochemical data she was diagnosed as a case of monogenic type of hypertension known as Liddle’s syndrome.Keywords: Paediatric Hypertension; Liddle’s Syndrome; Epithelial sodium channel (ENaC); Hypokalemia; Potassium sparing diuretics; Plasma Renin Activity (PRA)

Author Biographies

Danish Abdul Aziz, Aga Khan University Hospital Karachi, Pakistan


Fozia Memon, chief Resident Aga khan University Hospital

Chief ResidentDepartment of PaediatricsAKUH

Arshalooz Rahman, Aga Khan University Hospital Karachi Pakistan

Assistant ProfessorDepartment of Paediatrics and child HealthAKUH,KarachiPAkistan

Madiha Ali, Intern Aga khan University Hospital Karachi Pakistan

Intern House Physician Aga khan University HospitalKarachi, Pakistan


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