CONGENITAL SCAPHOID MEGALOURETHRA: REVISITING A RARE ANOMALY

Authors

  • Ilyas Zahoor Rehman Medical Institute Peshawar
  • Mohammad Asif Lady Reading Hospital Peshawar
  • Sarhad Khan Lady Reading Hospital Peshawar
  • Naveed Haroon Lady Reading Hospital

DOI:

https://doi.org/10.55519/JAMC-03-9596

Abstract

Megalourethra is an infrequent malformation of the anterior urethra that is caused by the lack of corpus sponigosum and in severe cases is accompanied by the lack of corpora cavernosa as well. We report a five-year-old boy presented to us with scaphoid variety of megalourethra having complaints of ballooning of urethra during voiding. He was investigated with urethrogram and cystoscopy and subsequently repaired with Nesbitt Longitudinal Reduction Urethroplasty. He had smooth recovery postoperatively with normal voiding stream on follow up. 

References

Zugor V, Schrott KM, Schott GE. A complex case of megalourethra and its repair. J Pediatr Urol 2006;2(6):592–5.

Mohan CG, Prakash SV, Kumar VV, Babu RG. Isolated megalourethra: A rare case report and review of literature. J Indian Assoc Pediatr Surg 2014;19(3):178–80.

Wax JR, Pinette MG, Landes A, Cartin A, Blackstone J. Prenatal Sonographic Diagnosis of Congenital Megalourethra With In Utero Spontaneous Resolution. J Ultrasound Med 2009;28(10):1385–8.

Advait P, Doshi B, Singh S, Parekh B. Congenital megalourethra: spectrum of presentation and insights in embryology and management. IntSurgJ 2016;2(4):660–4.

Sreetharan V, Sommerlad BC, Kangesu L. A case of congenital megalourethra. JPlast ReconstrAesthetSurg 2006;59(5):550–2.

Stephens FD, Fortune DW. Pathogenesis of megalourethra. J Urol 1993;149:1512–6.

Kulkarni AA, Gupta A, Kothari P,Jayaswal S, Dikshit V, Kekre G,et al. Congenital scaphoid megalourethra associated with posterior urethral valve: A case report. Ped Urol Case Rep 2018;5(1):13–5.

Nesbitt TE. Congenital megalourethra. J Urol 1955;73(5):839–42.

Amsalem H, Fitzgerald B, Keating S, Ryan G, Keunen J, Pippi Salle JL, et al. Congenital megalourethra: prenatal diagnosis and postnatal/autopsy findings in 10 cases. Ultrasound ObstetGynecol 2011;37(6):678–83.

Jones EA, Freedman AL, Ehrlich RM. Megalourethra and urethral diverticula. Urol Clin North Am 2002;29(2):341–8.

Moaddab A, Sananes N, Hernandez-Ruano S, Werneck Britto IS, Blumenfeld Y, Stoll F, et al. Prenatal diagnosis and perinatal outcomes of congenital megalourethra: a multicenter cohort study and systematic review of the literature. J Ultrasound Med 2015;34(11):2057–64.

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Published

2022-06-21

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