PAPILLON-LEFÈVRE SYNDROME

Abstract

A 9 years old male presented with keratotic plaques over the skin of his palms and soles extending onto the dorsal surface and swollen gums since the age of 4 with subsequent loss of most of his permanent dentition. These findings are consistent with Papillon-Lefèvre syndrome.Key words:    Papillon-Lefevre syndrome (PLS), palmar-plantar keratoderma, periodontitis, premature teeth loss